Overview
The G6PD gene encodes the enzyme glucose-6-phosphate dehydrogenase. It protects red blood cells from oxidative stress by providing NADPH.
Xq28 (X chromosome)
Metabolism
X-linked recessive
400+ million worldwide
Associated Diseases
-
🩸 Favism (G6PD Deficiency)
Acute hemolysis after consumption of fava beans or certain medications.
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🩸 Chronic Hemolysis
Rare variants lead to permanent anemia.
🧬 Relevant SNPs
X:154535202
/
Significance: G6PD A- variant. Common in Africa, leads to moderate enzyme deficiency.
X:154531389
/
Significance: G6PD Mediterranean. Severe form of deficiency, common in the Mediterranean region.
⚕️ Clinical Management
Avoidance of triggers (fava beans, primaquine, nitrofurantoin). Emergency medical ID card recommended.
📚 Data Sources
- Source: OMIM: #305900
- Source: dbSNP: rs1050828, rs5030868
- Source: WHO G6PD Guidelines
Biological Function
Associated Conditions
Analyzed Markers
Val68Met (G6PD A-) - Moderate deficiency (~10-60% activity). Common in Africa.
Ser188Phe (G6PD Mediterranean) - Severe deficiency (<10% activity). Common in the Mediterranean.
Arg459Leu (G6PD Canton) - Severe deficiency. Common in Southeast Asia.