Overview
BRCA2 is another important tumor suppressor gene, closely related to BRCA1, and playing a similar role in DNA repair.
13q13.1 (Chromosome 13)
Tumor Suppressor
Autosomal dominant
1:400 to 1:800
Function & Significance
BRCA2 is essential for homologous recombination, a major DNA repair mechanism. It works together with RAD51 to repair DNA double-strand breaks.
🔬 DNA Repair
BRCA2 plays a central role in repairing DNA double-strand breaks through homologous recombination. Mutations lead to:
- Genomic instability
- Increased mutation rate
- Carcinogenesis
Associated Diseases
-
🎗️ Hereditary Breast and Ovarian Cancer Syndrome
Up to 85% lifetime risk for breast cancer in mutation carriers
-
👨 Breast Cancer in Men
BRCA2 mutations also significantly increase the risk in men
-
🔬 Prostate Cancer
Increased risk for aggressive prostate cancer
-
🎯 Pancreatic Cancer
3-5 fold increased risk
🧬 Relevant SNPs (Single Nucleotide Polymorphisms)
Key pathogenic variants in BRCA2:
13:32913055
/
Significance: 6174delT – a common mutation in Ashkenazi Jews (~1% carrier rate). Leads to a truncated, non-functional protein.
13:32914437
/
Significance: Pathogenic variant in the DNA-binding domain. Impairs the ability to repair DNA.
Clinical Relevance
⚕️ Genetic Testing
BRCA2 testing is recommended in cases of:
- Familial clustering of breast or ovarian cancer
- Breast cancer in men
- Early onset of disease (< 50 years)
- Multiple primary tumors
💊 Management & Prevention
For BRCA2 mutation carriers:
- Intensified early detection (MRI, mammography)
- Prophylactic mastectomy (90% risk reduction)
- Prophylactic oophorectomy
- PARP inhibitors if cancer develops
- Regular prostate screenings (men)
📚 Data Sources
The information on this page is based on the following scientific sources:
- OMIM: #600185 – Online Mendelian Inheritance in Man
- ClinVar: Clinical Variant Database (NCBI)
- dbSNP: rs80359550, rs80359605 – SNP Database (NCBI)
- NCCN Guidelines: Genetic/Familial High-Risk Assessment
- PubMed: Peer-reviewed scientific literature
Last Update: February 2026
Biological Function
Associated Conditions
Analyzed Markers
6174delT - Common mutation in Ashkenazi Jews
Pathogenic variant in DNA binding domain